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Rho-kinase inactivation prolongs survival of an intermediate SMA mouse model

Human molecular genetics, 2010-04, Vol.19 (8), p.1468-1478

2010

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Suppression of the necroptotic cell death pathways improves survival in Smn2B/− mice

Frontiers in cellular neuroscience, 2022-08, Vol.16

2022

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The Smn-independent beneficial effects of trichostatin A on an intermediate mouse model of spinal muscular atrophy

PloS one, 2014-07, Vol.9 (7), p.e101225-e101225

2014

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SMN, profilin IIa and plastin 3: A link between the deregulation of actin dynamics and SMA pathogenesis

Molecular and cellular neuroscience, 2009-08, Vol.42 (1), p.66-74

2009

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The proteolipid protein promoter drives expression outside of the oligodendrocyte lineage during embryonic and early postnatal development

PloS one, 2011-05, Vol.6 (5), p.e19772-e19772

2011

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Abnormal fatty acid metabolism is a core component of spinal muscular atrophy

Annals of clinical and translational neurology, 2019-08, Vol.6 (8), p.1519-1532

2019

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Mouse survival motor neuron alleles that mimic SMN2 splicing and are inducible rescue embryonic lethality early in development but not late

PloS one, 2010-12, Vol.5 (12), p.e15887-e15887

2010

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Motor transmission defects with sex differences in a new mouse model of mild spinal muscular atrophy

EBioMedicine, 2020-05, Vol.55, p.102750-102750, Article 102750

2020

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Low fat diets increase survival of a mouse model of spinal muscular atrophy

Annals of clinical and translational neurology, 2019-11, Vol.6 (11), p.2340-2346

2019

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Splicing arrays reveal novel RBM10 targets, including SMN2 pre-mRNA

BMC molecular biology, 2017-07, Vol.18 (1), p.19-19, Article 19

2017

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Defects in neuromuscular junction remodelling in the Smn2B/− mouse model of spinal muscular atrophy

Neurobiology of disease, 2013-01, Vol.49, p.57-67

2013

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A novel whole-cell lysate kinase assay identifies substrates of the p38 MAPK in differentiating myoblasts

Skeletal muscle, 2012-03, Vol.2 (1), p.5-5, Article 5

2012

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Long term peripheral AAV9-SMN gene therapy promotes survival in a mouse model of spinal muscular atrophy

Human molecular genetics, 2024-02, Vol.33 (6), p.510-519

2024

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A critical smn threshold in mice dictates onset of an intermediate spinal muscular atrophy phenotype associated with a distinct neuromuscular junction pathology

Neuromuscular disorders : NMD, 2012-03, Vol.22 (3), p.263-276

2012

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Defects in neuromuscular junction remodelling in the Smn(2B/-) mouse model of spinal muscular atrophy

Neurobiology of disease, 2013-01, Vol.49, p.57-67

2013

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Defects in pancreatic development and glucose metabolism in SMN-depleted mice independent of canonical spinal muscular atrophy neuromuscular pathology

Human molecular genetics, 2014-07, Vol.23 (13), p.3432-3444

2014

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Central and peripheral delivered AAV9-SMN are both efficient but target different pathomechanisms in a mouse model of spinal muscular atrophy

Gene therapy, 2022-09, Vol.29 (9), p.544-554

2022

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The lamina-associated polypeptide 2 (LAP2) isoforms beta, gamma and omega of zebrafish: developmental expression and behavior during the cell cycle

Journal of cell science, 2003-06, Vol.116 (Pt 12), p.2505-2517

2003

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Glucose metabolism and pancreatic defects in spinal muscular atrophy

Annals of neurology, 2012-08, Vol.72 (2), p.256-268

2012

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Suppression of the necroptotic cell death pathways improves survival in Smn 2B/- mice

Frontiers in cellular neuroscience, 2022-01, Vol.16, p.972029-972029

2022

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Intramuscular adipogenesis is inhibited by myo-endothelial progenitors with functioning Bmpr1a signalling

Nature communications, 2014-06, Vol.5 (1), p.4063-4063, Article 4063

2014

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Transcriptional profiling of differentially vulnerable motor neurons at pre-symptomatic stage in the Smn (2b/-) mouse model of spinal muscular atrophy

Acta neuropathologica communications, 2015-09, Vol.3, p.55-55

2015

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G‐protein coupled receptor 56 promotes myoblast fusion through serum response factor‐ and nuclear factor of activated T‐cell‐mediated signalling but is not essential for muscle development in vivo

The FEBS journal, 2013-12, Vol.280 (23), p.6097-6113

2013

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Fam65b is important for formation of the HDAC6‐dysferlin protein complex during myogenic cell differentiation

The FASEB journal, 2014-07, Vol.28 (7), p.2955-2969

2014

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Blood Flow to the Spleen is Altered in a Mouse Model of Spinal Muscular Atrophy

Journal of neuromuscular diseases, 2020-01, Vol.7 (3), p.315-322

2020

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Rho-kinase inactivation prolongs survival of an intermediate SMA mouse model

Suppression of the necroptotic cell death pathways improves survival in Smn2B/− mice

The Smn-independent beneficial effects of trichostatin A on an intermediate mouse model of spinal muscular atrophy

SMN, profilin IIa and plastin 3: A link between the deregulation of actin dynamics and SMA pathogenesis

The proteolipid protein promoter drives expression outside of the oligodendrocyte lineage during embryonic and early postnatal development

Abnormal fatty acid metabolism is a core component of spinal muscular atrophy

Mouse survival motor neuron alleles that mimic SMN2 splicing and are inducible rescue embryonic lethality early in development but not late

Motor transmission defects with sex differences in a new mouse model of mild spinal muscular atrophy

Low fat diets increase survival of a mouse model of spinal muscular atrophy

Splicing arrays reveal novel RBM10 targets, including SMN2 pre-mRNA

Defects in neuromuscular junction remodelling in the Smn2B/− mouse model of spinal muscular atrophy

A novel whole-cell lysate kinase assay identifies substrates of the p38 MAPK in differentiating myoblasts

Long term peripheral AAV9-SMN gene therapy promotes survival in a mouse model of spinal muscular atrophy

A critical smn threshold in mice dictates onset of an intermediate spinal muscular atrophy phenotype associated with a distinct neuromuscular junction pathology

Defects in neuromuscular junction remodelling in the Smn(2B/-) mouse model of spinal muscular atrophy

Defects in pancreatic development and glucose metabolism in SMN-depleted mice independent of canonical spinal muscular atrophy neuromuscular pathology

Central and peripheral delivered AAV9-SMN are both efficient but target different pathomechanisms in a mouse model of spinal muscular atrophy

The lamina-associated polypeptide 2 (LAP2) isoforms beta, gamma and omega of zebrafish: developmental expression and behavior during the cell cycle

Glucose metabolism and pancreatic defects in spinal muscular atrophy

Suppression of the necroptotic cell death pathways improves survival in Smn 2B/- mice

Intramuscular adipogenesis is inhibited by myo-endothelial progenitors with functioning Bmpr1a signalling

Transcriptional profiling of differentially vulnerable motor neurons at pre-symptomatic stage in the Smn (2b/-) mouse model of spinal muscular atrophy

G‐protein coupled receptor 56 promotes myoblast fusion through serum response factor‐ and nuclear factor of activated T‐cell‐mediated signalling but is not essential for muscle development in vivo

Fam65b is important for formation of the HDAC6‐dysferlin protein complex during myogenic cell differentiation

Blood Flow to the Spleen is Altered in a Mouse Model of Spinal Muscular Atrophy

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