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Prion Strain Mutation and Selection

Science (American Association for the Advancement of Science), 2010-05, Vol.328 (5982), p.1111-1112

Collinge, John

2010

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Genetic Factors in Mammalian Prion Diseases

Annual review of genetics, 2019-12, Vol.53, p.117

2019

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Mammalian prions and their wider relevance in neurodegenerative diseases

Nature (London), 2016-11, Vol.539 (7628), p.217-226

Collinge, John

2016

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Distinct responses of neurons and astrocytes to TDP-43 proteinopathy in amyotrophic lateral sclerosis

Brain (London, England : 1878), 2020-02, Vol.143 (2), p.430-440

2020

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Prion propagation and toxicity in vivo occur in two distinct mechanistic phases

Nature (London), 2011-02, Vol.470 (7335), p.540-542

2011

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PrP is a central player in toxicity mediated by soluble aggregates of neurodegeneration-causing proteins

Acta neuropathologica, 2020-03, Vol.139 (3), p.503-526

2020

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A naturally occurring variant of the human prion protein completely prevents prion disease

Nature (London), 2015-06, Vol.522 (7557), p.478-481

2015

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Large C9orf72 Hexanucleotide Repeat Expansions Are Seen in Multiple Neurodegenerative Syndromes and Are More Frequent Than Expected in the UK Population

American journal of human genetics, 2013-03, Vol.92 (3), p.345-353

2013

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Structural features distinguishing infectious ex vivo mammalian prions from non-infectious fibrillar assemblies generated in vitro

Scientific reports, 2019-01, Vol.9 (1), p.376-376, Article 376

2019

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Two mouse models of Alzheimer’s disease accumulate amyloid at different rates and have distinct Aβ oligomer profiles unaltered by ablation of cellular prion protein

PloS one, 2023-11, Vol.18 (11), p.e0294465-e0294465

2023

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Depleting Neuronal PrP in Prion Infection Prevents Disease and Reverses Spongiosis

Science (American Association for the Advancement of Science), 2003-10, Vol.302 (5646), p.871-874

2003

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Single treatment with RNAi against prion protein rescues early neuronal dysfunction and prolongs survival in mice with prion disease

Proceedings of the National Academy of Sciences - PNAS, 2008-07, Vol.105 (29), p.10238-10243

2008

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Characterisation and prion transmission study in mice with genetic reduction of sporadic Creutzfeldt-Jakob disease risk gene Stx6

Neurobiology of disease, 2024-01, Vol.190, p.106363-106363, Article 106363

2024

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Targeting Cellular Prion Protein Reverses Early Cognitive Deficits and Neurophysiological Dysfunction in Prion-Infected Mice

Neuron (Cambridge, Mass.), 2007-02, Vol.53 (3), p.325-335

2007

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Homozygosity for the C9orf72 GGGGCC repeat expansion in frontotemporal dementia

Acta neuropathologica, 2013-09, Vol.126 (3), p.401-409

2013

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Disease-Associated Prion Protein Oligomers Inhibit the 26S Proteasome

Molecular cell, 2007-04, Vol.26 (2), p.175-188

2007

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FUS pathology defines the majority of tau- and TDP-43-negative frontotemporal lobar degeneration

Acta neuropathologica, 2010-07, Vol.120 (1), p.33-41

2010

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Prion protein gene M232R variation is probably an uncommon polymorphism rather than a pathogenic mutation

Brain (London, England : 1878), 2012-02, Vol.135 (2), p.e209-e209

2012

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Diagnosing Sporadic Creutzfeldt-Jakob Disease by the Detection of Abnormal Prion Protein in Patient Urine

JAMA neurology, 2016-12, Vol.73 (12), p.1454

2016

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A novel and rapid method for obtaining high titre intact prion strains from mammalian brain

Scientific reports, 2015-05, Vol.5 (1), p.10062-10062, Article 10062

2015

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Progressive neuronal inclusion formation and axonal degeneration in CHMP2B mutant transgenic mice

Brain (London, England : 1878), 2012-03, Vol.135 (Pt 3), p.819-832

2012

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Location and Properties of Metal-Binding Sites on the Human Prion Protein

Proceedings of the National Academy of Sciences - PNAS, 2001-07, Vol.98 (15), p.8531-8535

2001

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Genome-wide association study in multiple human prion diseases suggests genetic risk factors additional to PRNP

Human molecular genetics, 2012-04, Vol.21 (8), p.1897-1906

2012

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The role of CHMP2B in frontotemporal dementia

Biochemical Society transactions, 2009-02, Vol.37 (Pt 1), p.208

2009

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Prion Strain Mutation and Selection

Genetic Factors in Mammalian Prion Diseases

Mammalian prions and their wider relevance in neurodegenerative diseases

Distinct responses of neurons and astrocytes to TDP-43 proteinopathy in amyotrophic lateral sclerosis

Prion propagation and toxicity in vivo occur in two distinct mechanistic phases

PrP is a central player in toxicity mediated by soluble aggregates of neurodegeneration-causing proteins

A naturally occurring variant of the human prion protein completely prevents prion disease

Large C9orf72 Hexanucleotide Repeat Expansions Are Seen in Multiple Neurodegenerative Syndromes and Are More Frequent Than Expected in the UK Population

Structural features distinguishing infectious ex vivo mammalian prions from non-infectious fibrillar assemblies generated in vitro

Two mouse models of Alzheimer’s disease accumulate amyloid at different rates and have distinct Aβ oligomer profiles unaltered by ablation of cellular prion protein

Depleting Neuronal PrP in Prion Infection Prevents Disease and Reverses Spongiosis

Single treatment with RNAi against prion protein rescues early neuronal dysfunction and prolongs survival in mice with prion disease

Characterisation and prion transmission study in mice with genetic reduction of sporadic Creutzfeldt-Jakob disease risk gene Stx6

Targeting Cellular Prion Protein Reverses Early Cognitive Deficits and Neurophysiological Dysfunction in Prion-Infected Mice

Homozygosity for the C9orf72 GGGGCC repeat expansion in frontotemporal dementia

Disease-Associated Prion Protein Oligomers Inhibit the 26S Proteasome

FUS pathology defines the majority of tau- and TDP-43-negative frontotemporal lobar degeneration

Prion protein gene M232R variation is probably an uncommon polymorphism rather than a pathogenic mutation

Diagnosing Sporadic Creutzfeldt-Jakob Disease by the Detection of Abnormal Prion Protein in Patient Urine

A novel and rapid method for obtaining high titre intact prion strains from mammalian brain

Progressive neuronal inclusion formation and axonal degeneration in CHMP2B mutant transgenic mice

Clinical Trial Simulations Based on Genetic Stratification and the Natural History of a Functional Outcome Measure in Creutzfeldt-Jakob Disease

Location and Properties of Metal-Binding Sites on the Human Prion Protein

Genome-wide association study in multiple human prion diseases suggests genetic risk factors additional to PRNP

The role of CHMP2B in frontotemporal dementia

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