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Correlations Between Serum Cholesterol and Vascular Lesions in Fabry Disease Patients

Circulation Journal, 2018/11/24, Vol.82(12), pp.3058-3063

2018

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Extension of PREMIER combustion operation range using split micro pilot fuel injection in a dual fuel natural gas compression ignition engine: A performance-based and visual investigation

Fuel (Guildford), 2016-12, Vol.185, p.243-253

2016

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End-gas autoignition characteristics of PREMIER combustion in a pilot fuel-ignited dual-fuel biogas engine

Fuel (Guildford), 2019-10, Vol.254, p.115634, Article 115634

2019

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Laser-induced plasma generation and evolution in a transient spray

Optics express, 2014-01, Vol.22 (S1), p.A44

2014

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Combustion characteristics of wet ethanol ignited using a focused Q-switched Nd:YAG nanosecond laser

Fuel (Guildford), 2016-02, Vol.165, p.331-340

2016

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Efficacy and safety of enzyme-replacement-therapy with agalsidase alfa in 36 treatment-naïve Fabry disease patients

BMC pharmacology & toxicology, 2017-06, Vol.18 (1), p.43-43, Article 43

2017

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Effect of ambient pressure on local concentration measurement of transient hydrogen jet in a constant-volume vessel using spark-induced breakdown spectroscopy

International journal of hydrogen energy, 2015-04, Vol.40 (13), p.4717-4725

2015

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Visualization and concentration measurement of a direct-injection hydrogen jet in a constant-volume vessel using spark-induced breakdown spectroscopy

International journal of hydrogen energy, 2014-10, Vol.39 (31), p.17896-17905

2014

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Otological aspects of Fabry disease in patients with normal hearing

Nagoya journal of medical science, 2019-08, Vol.81 (3), p.469-475

2019

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Detection of novel Fabry disease‐associated pathogenic variants in Japanese patients by newborn and high‐risk screening

Molecular genetics & genomic medicine, 2020-11, Vol.8 (11), p.e1502-n/a

2020

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Potential prognostic implications of myocardial thallium-201 and iodine-123-beta-methylpentadecanoic acid dual scintigraphy in patients with Anderson–Fabry disease

Annals of nuclear medicine, 2019-12, Vol.33 (12), p.930-936

2019

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Descriptive epidemiology of Fabry disease among beneficiaries of the Specified Disease Treatment Research Program in Japan

Journal of epidemiology, 2012, Vol.22 (4), p.370-374

2012

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Combustion characteristics and NOX emissions of biogas fuels with various CO2 contents in a micro co-generation spark-ignition engine

Applied energy, 2016-11, Vol.182, p.539-547

2016

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Clinical course of patients with Fabry disease who were switched from agalsidase-β to agalsidase-α

Genetics in medicine, 2014-10, Vol.16 (10), p.766-772

2014

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Differences between PREMIER combustion in a natural gas spark-ignition engine and knocking with pressure oscillations

Proceedings of the Combustion Institute, 2019, Vol.37 (4), p.4983-4991

2019

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Performance, emissions and end-gas autoignition characteristics of PREMIER combustion in a pilot fuel-ignited dual-fuel biogas engine with various CO2 ratios

Fuel (Guildford), 2021-02, Vol.286, p.119330, Article 119330

2021

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Laser-induced plasma generation and evolution in a transient spray

Optics express, 2014-01, Vol.22 Suppl 1, p.A44-A52

2014

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Evaluation of the Flame Lift-off Length in Diesel Spray Combustion Based on Flame Extinction

Journal of Thermal Science and Technology, 2010, Vol.5(2), pp.238-251

2010

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Clinical observation of patients with Fabry disease after switching from agalsidase beta (Fabrazyme) to agalsidase alfa (Replagal)

Genetics in medicine, 2012-09, Vol.14 (9), p.779-786

2012

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Prevalence of patients with lysosomal storage disorders and peroxisomal disorders: A nationwide survey in Japan

Molecular genetics and metabolism, 2021-07, Vol.133 (3), p.277-288

2021

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Clinical course of 13 patients with Fabry disease switching from agalsidase-α to agalsidase-β and who were followed for 36 months

Molecular genetics and metabolism, 2013-02, Vol.108 (2), p.S93-S93

2013

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Clinical course of 13 patients with Fabry disease switching from agalsidase-α to agalsidase-β and who were followed for 36months

Molecular genetics and metabolism, 2013-02, Vol.108 (2), p.S93

2013

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Correlations Between Serum Cholesterol and Vascular Lesions in Fabry Disease Patients

Circulation Journal, 2018, pp.CJ-18-0378

2018

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Multidimensional CFD simulation of syngas combustion in a micro-pilot-ignited dual-fuel engine using a constructed chemical kinetics mechanism

International journal of hydrogen energy, 2011-10, Vol.36 (21), p.13793-13807

2011

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An Analysis of Local Quantities of Turbulent Premixed Flames Using DNS Databases

Journal of Thermal Science and Technology, 2008, Vol.3(1), pp.103-111

2008

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Correlations Between Serum Cholesterol and Vascular Lesions in Fabry Disease Patients

Extension of PREMIER combustion operation range using split micro pilot fuel injection in a dual fuel natural gas compression ignition engine: A performance-based and visual investigation

End-gas autoignition characteristics of PREMIER combustion in a pilot fuel-ignited dual-fuel biogas engine

Laser-induced plasma generation and evolution in a transient spray

Combustion characteristics of wet ethanol ignited using a focused Q-switched Nd:YAG nanosecond laser

Efficacy and safety of enzyme-replacement-therapy with agalsidase alfa in 36 treatment-naïve Fabry disease patients

Effect of ambient pressure on local concentration measurement of transient hydrogen jet in a constant-volume vessel using spark-induced breakdown spectroscopy

Visualization and concentration measurement of a direct-injection hydrogen jet in a constant-volume vessel using spark-induced breakdown spectroscopy

Otological aspects of Fabry disease in patients with normal hearing

Detection of novel Fabry disease‐associated pathogenic variants in Japanese patients by newborn and high‐risk screening

Potential prognostic implications of myocardial thallium-201 and iodine-123-beta-methylpentadecanoic acid dual scintigraphy in patients with Anderson–Fabry disease

Descriptive epidemiology of Fabry disease among beneficiaries of the Specified Disease Treatment Research Program in Japan

Combustion characteristics and NOX emissions of biogas fuels with various CO2 contents in a micro co-generation spark-ignition engine

Clinical course of patients with Fabry disease who were switched from agalsidase-β to agalsidase-α

Differences between PREMIER combustion in a natural gas spark-ignition engine and knocking with pressure oscillations

Performance, emissions and end-gas autoignition characteristics of PREMIER combustion in a pilot fuel-ignited dual-fuel biogas engine with various CO2 ratios

Laser-induced plasma generation and evolution in a transient spray

Evaluation of the Flame Lift-off Length in Diesel Spray Combustion Based on Flame Extinction

Clinical observation of patients with Fabry disease after switching from agalsidase beta (Fabrazyme) to agalsidase alfa (Replagal)

Prevalence of patients with lysosomal storage disorders and peroxisomal disorders: A nationwide survey in Japan

Clinical course of 13 patients with Fabry disease switching from agalsidase-α to agalsidase-β and who were followed for 36 months

Clinical course of 13 patients with Fabry disease switching from agalsidase-α to agalsidase-β and who were followed for 36months

Correlations Between Serum Cholesterol and Vascular Lesions in Fabry Disease Patients

Multidimensional CFD simulation of syngas combustion in a micro-pilot-ignited dual-fuel engine using a constructed chemical kinetics mechanism

An Analysis of Local Quantities of Turbulent Premixed Flames Using DNS Databases

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