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Method for quantitative study of airway functional microanatomy using micro-optical coherence tomography

PloS one, 2013-01, Vol.8 (1), p.e54473-e54473

2013

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From CFTR biology toward combinatorial pharmacotherapy: expanded classification of cystic fibrosis mutations

Molecular biology of the cell, 2016-02, Vol.27 (3), p.424-433

2016

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A pharmacologic approach to acquired cystic fibrosis transmembrane conductance regulator dysfunction in smoking related lung disease

PloS one, 2012-06, Vol.7 (6), p.e39809-e39809

2012

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A small molecule that induces translational readthrough of CFTR nonsense mutations by eRF1 depletion

Nature communications, 2021-07, Vol.12 (1), p.4358-4358, Article 4358

2021

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Mutation accumulation in H. sapiens F508del CFTR countermands dN/dS type genomic analysis

PloS one, 2024-07, Vol.19 (7), p.e0305832

2024

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Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats

PloS one, 2014-03, Vol.9 (3), p.e91253

2014

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Ivacaftor Reverses Airway Mucus Abnormalities in a Rat Model Harboring a Humanized G551D-CFTR

American journal of respiratory and critical care medicine, 2020-11, Vol.202 (9), p.1271-1282

2020

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Translation velocity determines the efficacy of engineered suppressor tRNAs on pathogenic nonsense mutations

Nature communications, 2024-04, Vol.15 (1), p.2957-2957, Article 2957

2024

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Relationships between genomic dissipation and de novo SNP evolution

PloS one, 2024-05, Vol.19 (5), p.e0303257-e0303257

2024

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Myofibroblast differentiation and enhanced TGF-B signaling in cystic fibrosis lung disease

PloS one, 2013-08, Vol.8 (8), p.e70196-e70196

2013

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Targeted correction and restored function of the CFTR gene in cystic fibrosis induced pluripotent stem cells

Stem cell reports, 2015-04, Vol.4 (4), p.569-577

2015

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Robust Stimulation of W1282X-CFTR Channel Activity by a Combination of Allosteric Modulators

PloS one, 2016-03, Vol.11 (3), p.e0152232-e0152232

2016

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Use of E. coli Purine Nucleoside Phosphorylase in the Treatment of Solid Tumors

Current pharmaceutical design, 2017-11, Vol.23 (45), p.7003-7024

2017

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Sinupret activates CFTR and TMEM16A-dependent transepithelial chloride transport and improves indicators of mucociliary clearance

PloS one, 2014-08, Vol.9 (8), p.e104090-e104090

2014

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Trafficking and function of the cystic fibrosis transmembrane conductance regulator: a complex network of posttranslational modifications

American journal of physiology. Lung cellular and molecular physiology, 2016-10, Vol.311 (4), p.L719-L733

2016

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Reduced bone length, growth plate thickness, bone content, and IGF-I as a model for poor growth in the CFTR-deficient rat

PloS one, 2017-11, Vol.12 (11), p.e0188497-e0188497

2017

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A medium composition containing normal resting glucose that supports differentiation of primary human airway cells

Scientific reports, 2022-01, Vol.12 (1), p.1540-15, Article 1540

2022

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Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis

Nature chemical biology, 2010-01, Vol.6 (1), p.25-33

2010

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Assessing cell-specific effects of genetic variations using tRNA microarrays

BMC genomics, 2019-07, Vol.20 (Suppl 8), p.549-549, Article 549

2019

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Ribosomal Stalk Protein Silencing Partially Corrects the ΔF508-CFTR Functional Expression Defect

PLoS biology, 2016-05, Vol.14 (5), p.e1002462-e1002462

2016

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Cigarette smoke condensate inhibits transepithelial chloride transport and ciliary beat frequency

The Laryngoscope, 2009-11, Vol.119 (11), p.2269-2274

2009

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Targeted Gene Insertion for Functional CFTR Restoration in Airway Epithelium

Frontiers in genome editing, 2022-03, Vol.4, p.847645

2022

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Resveratrol enhances airway surface liquid depth in sinonasal epithelium by increasing cystic fibrosis transmembrane conductance regulator open probability

PloS one, 2013-11, Vol.8 (11), p.e81589-e81589

2013

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LPS decreases CFTR open probability and mucociliary transport through generation of reactive oxygen species

Redox biology, 2021-07, Vol.43, p.101998-101998, Article 101998

2021

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Increasing the Endoplasmic Reticulum Pool of the F508del Allele of the Cystic Fibrosis Transmembrane Conductance Regulator Leads to Greater Folding Correction by Small Molecule Therapeutics

PloS one, 2016-10, Vol.11 (10), p.e0163615-e0163615

2016

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Method for quantitative study of airway functional microanatomy using micro-optical coherence tomography

From CFTR biology toward combinatorial pharmacotherapy: expanded classification of cystic fibrosis mutations

A pharmacologic approach to acquired cystic fibrosis transmembrane conductance regulator dysfunction in smoking related lung disease

A small molecule that induces translational readthrough of CFTR nonsense mutations by eRF1 depletion

Mutation accumulation in H. sapiens F508del CFTR countermands dN/dS type genomic analysis

Characterization of defects in ion transport and tissue development in cystic fibrosis transmembrane conductance regulator (CFTR)-knockout rats

Ivacaftor Reverses Airway Mucus Abnormalities in a Rat Model Harboring a Humanized G551D-CFTR

Translation velocity determines the efficacy of engineered suppressor tRNAs on pathogenic nonsense mutations

Relationships between genomic dissipation and de novo SNP evolution

Myofibroblast differentiation and enhanced TGF-B signaling in cystic fibrosis lung disease

Targeted correction and restored function of the CFTR gene in cystic fibrosis induced pluripotent stem cells

Robust Stimulation of W1282X-CFTR Channel Activity by a Combination of Allosteric Modulators

Use of E. coli Purine Nucleoside Phosphorylase in the Treatment of Solid Tumors

Sinupret activates CFTR and TMEM16A-dependent transepithelial chloride transport and improves indicators of mucociliary clearance

Trafficking and function of the cystic fibrosis transmembrane conductance regulator: a complex network of posttranslational modifications

Reduced bone length, growth plate thickness, bone content, and IGF-I as a model for poor growth in the CFTR-deficient rat

A medium composition containing normal resting glucose that supports differentiation of primary human airway cells

Reduced histone deacetylase 7 activity restores function to misfolded CFTR in cystic fibrosis

Assessing cell-specific effects of genetic variations using tRNA microarrays

Ribosomal Stalk Protein Silencing Partially Corrects the ΔF508-CFTR Functional Expression Defect

Cigarette smoke condensate inhibits transepithelial chloride transport and ciliary beat frequency

Targeted Gene Insertion for Functional CFTR Restoration in Airway Epithelium

Resveratrol enhances airway surface liquid depth in sinonasal epithelium by increasing cystic fibrosis transmembrane conductance regulator open probability

LPS decreases CFTR open probability and mucociliary transport through generation of reactive oxygen species

Increasing the Endoplasmic Reticulum Pool of the F508del Allele of the Cystic Fibrosis Transmembrane Conductance Regulator Leads to Greater Folding Correction by Small Molecule Therapeutics

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