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Recombinant ADAMTS-13: first-in-human pharmacokinetics and safety in congenital thrombotic thrombocytopenic purpura

Blood, 2017-11, Vol.130 (19), p.2055-2063

2017

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The International Hereditary Thrombotic Thrombocytopenic Purpura Registry: key findings at enrollment until 2017

Haematologica (Roma), 2019-10, Vol.104 (10), p.2107-2115

2019

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Shear-Induced Unfolding and Enzymatic Cleavage of Full-Length VWF Multimers

Biophysical journal, 2016-02, Vol.110 (3), p.545-554

2016

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Nonsense mutation and inactivation of SMARCA4 (BRG1) in an atypical teratoid/rhabdoid tumor showing retained SMARCB1 (INI1) expression

The American journal of surgical pathology, 2011-06, Vol.35 (6), p.933-935

2011

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High-resolution genomic analysis suggests the absence of recurrent genomic alterations other than SMARCB1 aberrations in atypical teratoid/rhabdoid tumors

Genes chromosomes & cancer, 2013-02, Vol.52 (2), p.185-190

2013

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Interaction of von Willebrand factor domains with collagen investigated by single molecule force spectroscopy

The Journal of chemical physics, 2018-03, Vol.148 (12), p.123310-123310

2018

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Upshaw-Schulman syndrome-associated ADAMTS13 variants possess proteolytic activity at the surface of endothelial cells and in simulated circulation

PloS one, 2020-05, Vol.15 (5), p.e0232637-e0232637

2020

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Germline variants in SMARCB1 and other members of the BAF chromatin-remodeling complex across human disease entities: a meta-analysis

European journal of human genetics : EJHG, 2018-08, Vol.26 (8), p.1083-1093

2018

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von Willebrand factor is dimerized by protein disulfide isomerase

Blood, 2016-03, Vol.127 (9), p.1183-1191

2016

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Sellar Region Atypical Teratoid/Rhabdoid Tumors (ATRT) in Adults Display DNA Methylation Profiles of the ATRT-MYC Subgroup

The American journal of surgical pathology, 2018-04, Vol.42 (4), p.506-511

2018

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Force sensing by the vascular protein von Willebrand factor is tuned by a strong intermonomer interaction

Proceedings of the National Academy of Sciences - PNAS, 2016-02, Vol.113 (5), p.1208-1213

2016

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VWF propeptide and ratios between VWF, VWF propeptide, and FVIII in the characterization of type 1 von Willebrand disease

Blood, 2013-03, Vol.121 (12), p.2336-2339

2013

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Advancing multimer analysis of von Willebrand factor by single-molecule AFM imaging

PloS one, 2019-01, Vol.14 (1), p.e0210963-e0210963

2019

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Small cell undifferentiated (SCUD) hepatoblastomas: All malignant rhabdoid tumors?

Genes chromosomes & cancer, 2016-12, Vol.55 (12), p.925-931

2016

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The von Willebrand factor Tyr2561 allele is a gain-of-function variant and a risk factor for early myocardial infarction

Blood, 2019-01, Vol.133 (4), p.356-365

2019

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Loss of SMARCB1/INI1 expression in poorly differentiated chordomas

Acta neuropathologica, 2010-12, Vol.120 (6), p.745-753

2010

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Performance evaluation and multicentre study of a von Willebrand factor activity assay based on GPIb binding in the absence of ristocetin

Blood coagulation & fibrinolysis, 2014-12, Vol.25 (8), p.860-870

2014

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von Willebrand disease type 2A phenotypes IIC, IID and IIE: A day in the life of shear-stressed mutant von Willebrand factor

Thrombosis and haemostasis, 2014, Vol.112 (1), p.96-108

2014

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Genetic and Clinical Predictors of Left Atrial Thrombus: A Single Center Case-Control Study

Clinical and applied thrombosis/hemostasis, 2021, Vol.27, p.10760296211021171-10760296211021171

2021

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pH-Dependent Interactions in Dimers Govern the Mechanics and Structure of von Willebrand Factor

Biophysical journal, 2016-07, Vol.111 (2), p.312-322

2016

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Von Willebrand Factor Mediates Pneumococcal Aggregation and Adhesion in Blood Flow

Frontiers in microbiology, 2019-03, Vol.10, p.511-511

2019

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Inflammation-associated ADAMTS13 deficiency promotes formation of ultra-large von Willebrand factor

Haematologica (Roma), 2008-01, Vol.93 (1), p.137-140

2008

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Improved 6‐year overall survival in AT/RT – results of the registry study Rhabdoid 2007

Cancer medicine (Malden, MA), 2016-08, Vol.5 (8), p.1765-1775

2016

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Laboratory Testing for von Willebrand Disease: Contribution of Multimer Analysis to Diagnosis and Classification

Seminars in thrombosis and hemostasis, 2006-07, Vol.32 (5), p.514-521

2006

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Update on von Willebrand factor multimers: focus on high-molecular-weight multimers and their role in hemostasis

Blood coagulation & fibrinolysis, 2014-04, Vol.25 (3), p.206-216

2014

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Recombinant ADAMTS-13: first-in-human pharmacokinetics and safety in congenital thrombotic thrombocytopenic purpura

The International Hereditary Thrombotic Thrombocytopenic Purpura Registry: key findings at enrollment until 2017

Shear-Induced Unfolding and Enzymatic Cleavage of Full-Length VWF Multimers

Nonsense mutation and inactivation of SMARCA4 (BRG1) in an atypical teratoid/rhabdoid tumor showing retained SMARCB1 (INI1) expression

High-resolution genomic analysis suggests the absence of recurrent genomic alterations other than SMARCB1 aberrations in atypical teratoid/rhabdoid tumors

Interaction of von Willebrand factor domains with collagen investigated by single molecule force spectroscopy

Upshaw-Schulman syndrome-associated ADAMTS13 variants possess proteolytic activity at the surface of endothelial cells and in simulated circulation

Germline variants in SMARCB1 and other members of the BAF chromatin-remodeling complex across human disease entities: a meta-analysis

von Willebrand factor is dimerized by protein disulfide isomerase

Sellar Region Atypical Teratoid/Rhabdoid Tumors (ATRT) in Adults Display DNA Methylation Profiles of the ATRT-MYC Subgroup

Force sensing by the vascular protein von Willebrand factor is tuned by a strong intermonomer interaction

VWF propeptide and ratios between VWF, VWF propeptide, and FVIII in the characterization of type 1 von Willebrand disease

Advancing multimer analysis of von Willebrand factor by single-molecule AFM imaging

Small cell undifferentiated (SCUD) hepatoblastomas: All malignant rhabdoid tumors?

The von Willebrand factor Tyr2561 allele is a gain-of-function variant and a risk factor for early myocardial infarction

Loss of SMARCB1/INI1 expression in poorly differentiated chordomas

Performance evaluation and multicentre study of a von Willebrand factor activity assay based on GPIb binding in the absence of ristocetin

von Willebrand disease type 2A phenotypes IIC, IID and IIE: A day in the life of shear-stressed mutant von Willebrand factor

Genetic and Clinical Predictors of Left Atrial Thrombus: A Single Center Case-Control Study

pH-Dependent Interactions in Dimers Govern the Mechanics and Structure of von Willebrand Factor

Von Willebrand Factor Mediates Pneumococcal Aggregation and Adhesion in Blood Flow

Inflammation-associated ADAMTS13 deficiency promotes formation of ultra-large von Willebrand factor

Improved 6‐year overall survival in AT/RT – results of the registry study Rhabdoid 2007

Laboratory Testing for von Willebrand Disease: Contribution of Multimer Analysis to Diagnosis and Classification

Update on von Willebrand factor multimers: focus on high-molecular-weight multimers and their role in hemostasis

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