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Anaplerotic treatment of long-chain fat oxidation disorders with triheptanoin: Review of 15 years Experience

Molecular genetics and metabolism, 2015-12, Vol.116 (4), p.260-268

2015

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Anaplerotic triheptanoin diet enhances mitochondrial substrate use to remodel the metabolome and improve lifespan, motor function, and sociability in MeCP2-null mice

PloS one, 2014-10, Vol.9 (10), p.e109527-e109527

2014

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Maximum dose, safety, tolerability and ketonemia after triheptanoin in glucose transporter type 1 deficiency (G1D)

Scientific reports, 2023-03, Vol.13 (1), p.3465-3465, Article 3465

2023

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Pyruvate carboxylase deficiency: Mechanisms, mimics and anaplerosis

Molecular genetics and metabolism, 2010-09, Vol.101 (1), p.9-17

2010

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Anaplerotic molecules: Current and future

Journal of inherited metabolic disease, 2006-04, Vol.29 (2-3), p.327-331

2006

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On stress-state dependent plasticity modeling: Significance of the hydrostatic stress, the third invariant of stress deviator and the non-associated flow rule

International journal of plasticity, 2011-02, Vol.27 (2), p.217-231

2011

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A Study on the Effect of the Stress State on Ductile Fracture

International journal of damage mechanics, 2010-01, Vol.19 (1), p.75-94

2010

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Triheptanoin for glucose transporter type I deficiency (G1D): modulation of human ictogenesis, cerebral metabolic rate, and cognitive indices by a food supplement

JAMA neurology, 2014-10, Vol.71 (10), p.1255

2014

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The safety assessment of Pythium irregulare as a producer of biomass and eicosapentaenoic acid for use in dietary supplements and food ingredients

Applied microbiology and biotechnology, 2013-09, Vol.97 (17), p.7579-7585

2013

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Treatment of cardiomyopathy and rhabdomyolysis in long-chain fat oxidation disorders using an anaplerotic odd-chain triglyceride

The Journal of clinical investigation, 2002-07, Vol.110 (2), p.259-269

2002

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Anaplerotic diet therapy in inherited metabolic disease: Therapeutic potential

Journal of inherited metabolic disease, 2006-04, Vol.29 (2-3), p.332-340

2006

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Systemic metabolic abnormalities in adult-onset acid maltase deficiency: beyond muscle glycogen accumulation

JAMA neurology, 2013-06, Vol.70 (6), p.756

2013

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Effects of a flotation vest and water flow rate on limb kinematics of Siberian Huskies swimming against a current

American journal of veterinary research, 2021-12, Vol.82 (12), p.955-962

2021

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Adult Polyglucosan Body Disease (APBD): Anaplerotic diet therapy (Triheptanoin) and demonstration of defective methylation pathways

Molecular genetics and metabolism, 2010-10, Vol.101 (2-3), p.246-252

2010

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Interrelations between C4 Ketogenesis, C5 Ketogenesis, and Anaplerosis in the Perfused Rat Liver

The Journal of biological chemistry, 2009-10, Vol.284 (41), p.27799-27807

2009

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Improving high soy feed formulations for the Florida pompano Trachinotus carolinus through newer soy products and carbohydrase supplementation

Journal of the World Aquaculture Society, 2019-04, Vol.50 (2), p.406-419

2019

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Parenteral and enteral metabolism of anaplerotic triheptanoin in normal rats. II. Effects on lipolysis, glucose production, and liver acyl-CoA profile

American journal of physiology: endocrinology and metabolism, 2010-02, Vol.298 (2), p.E362-E371

2010

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Pyruvate carboxylase deficiency: clinical and biochemical response to anaplerotic diet therapy

Molecular genetics and metabolism, 2005-04, Vol.84 (4), p.305-312

2005

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Short-chain acyl-CoA dehydrogenase gene mutation (c.319C>T) presents with clinical heterogeneity and is candidate founder mutation in individuals of Ashkenazi Jewish origin

Molecular genetics and metabolism, 2008-02, Vol.93 (2), p.179-189

2008

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Choice of oils for essential fat supplements can enhance production of abnormal metabolites in fat oxidation disorders

Molecular genetics and metabolism, 2007-12, Vol.92 (4), p.346-350

2007

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Parenteral and enteral metabolism of anaplerotic triheptanoin in normal rats

American journal of physiology: endocrinology and metabolism, 2006-10, Vol.291 (4), p.E860-E866

2006

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An investigation of the loading rate dependence of the Weibull stress parameters

Engineering fracture mechanics, 2008-04, Vol.75 (6), p.1451-1467

2008

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Effect of dietary fats with odd or even numbers of carbon atoms on metabolic response and muscle damage with exercise in Quarter Horse-type horses with type 1 polysaccharide storage myopathy

American journal of veterinary research, 2010-03, Vol.71 (3), p.326-336

2010

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Crack arrest testing of high strength structural steels for naval applications

Engineering fracture mechanics, 2009-02, Vol.76 (3), p.402-418

2009

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Effects of the stress state on plasticity and ductile failure of an aluminum 5083 alloy

International journal of plasticity, 2009-12, Vol.25 (12), p.2366-2382

2009

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Anaplerotic treatment of long-chain fat oxidation disorders with triheptanoin: Review of 15 years Experience

Anaplerotic triheptanoin diet enhances mitochondrial substrate use to remodel the metabolome and improve lifespan, motor function, and sociability in MeCP2-null mice

Maximum dose, safety, tolerability and ketonemia after triheptanoin in glucose transporter type 1 deficiency (G1D)

Pyruvate carboxylase deficiency: Mechanisms, mimics and anaplerosis

Anaplerotic molecules: Current and future

On stress-state dependent plasticity modeling: Significance of the hydrostatic stress, the third invariant of stress deviator and the non-associated flow rule

A Study on the Effect of the Stress State on Ductile Fracture

Triheptanoin for glucose transporter type I deficiency (G1D): modulation of human ictogenesis, cerebral metabolic rate, and cognitive indices by a food supplement

The safety assessment of Pythium irregulare as a producer of biomass and eicosapentaenoic acid for use in dietary supplements and food ingredients

Treatment of cardiomyopathy and rhabdomyolysis in long-chain fat oxidation disorders using an anaplerotic odd-chain triglyceride

Anaplerotic diet therapy in inherited metabolic disease: Therapeutic potential

Systemic metabolic abnormalities in adult-onset acid maltase deficiency: beyond muscle glycogen accumulation

Effects of a flotation vest and water flow rate on limb kinematics of Siberian Huskies swimming against a current

Adult Polyglucosan Body Disease (APBD): Anaplerotic diet therapy (Triheptanoin) and demonstration of defective methylation pathways

Interrelations between C4 Ketogenesis, C5 Ketogenesis, and Anaplerosis in the Perfused Rat Liver

Improving high soy feed formulations for the Florida pompano Trachinotus carolinus through newer soy products and carbohydrase supplementation

Parenteral and enteral metabolism of anaplerotic triheptanoin in normal rats. II. Effects on lipolysis, glucose production, and liver acyl-CoA profile

Pyruvate carboxylase deficiency: clinical and biochemical response to anaplerotic diet therapy

Short-chain acyl-CoA dehydrogenase gene mutation (c.319C>T) presents with clinical heterogeneity and is candidate founder mutation in individuals of Ashkenazi Jewish origin

Choice of oils for essential fat supplements can enhance production of abnormal metabolites in fat oxidation disorders

Parenteral and enteral metabolism of anaplerotic triheptanoin in normal rats

An investigation of the loading rate dependence of the Weibull stress parameters

Effect of dietary fats with odd or even numbers of carbon atoms on metabolic response and muscle damage with exercise in Quarter Horse-type horses with type 1 polysaccharide storage myopathy

Crack arrest testing of high strength structural steels for naval applications

Effects of the stress state on plasticity and ductile failure of an aluminum 5083 alloy

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