UB Paderborn / Katalog / Suche / in CDI

1 – 25 von 197

Sortiert nach

Evidence for a Superoxide Permeability Pathway in Endosomal Membranes

Molecular and Cellular Biology, 2008-06, Vol.28 (11), p.3700-3712

2008

Link zum Volltext

Verfügbarkeit prüfen

Directed differentiation of cholangiocytes from human pluripotent stem cells

Nature biotechnology, 2015-08, Vol.33 (8), p.853-861

2015

Link zum Volltext

Verfügbarkeit prüfen

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Potentiator VX-770 (Ivacaftor) Opens the Defective Channel Gate of Mutant CFTR in a Phosphorylation-dependent but ATP-independent Manner

The Journal of biological chemistry, 2012-10, Vol.287 (44), p.36639-36649

2012

Link zum Volltext

Verfügbarkeit prüfen

ORKAMBI-Mediated Rescue of Mucociliary Clearance in Cystic Fibrosis Primary Respiratory Cultures Is Enhanced by Arginine Uptake, Arginase Inhibition, and Promotion of Nitric Oxide Signaling to the Cystic Fibrosis Transmembrane Conductance Regulator Channel

Molecular pharmacology, 2019-10, Vol.96 (4), p.515-525

2019

Link zum Volltext

Verfügbarkeit prüfen

Efficient generation of functional CFTR-expressing airway epithelial cells from human pluripotent stem cells

Nature protocols, 2015-03, Vol.10 (3), p.363-381

2015

Link zum Volltext

Verfügbarkeit prüfen

Activity of a novel antimicrobial peptide against Pseudomonas aeruginosa biofilms

Scientific reports, 2018-10, Vol.8 (1), p.14728-12, Article 14728

2018

Link zum Volltext

Verfügbarkeit prüfen

Acellular Lung Scaffolds Direct Differentiation of Endoderm to Functional Airway Epithelial Cells: Requirement of Matrix-Bound HS Proteoglycans

Stem cell reports, 2015-03, Vol.4 (3), p.419-430

2015

Link zum Volltext

Verfügbarkeit prüfen

Generation of functional ciliated cholangiocytes from human pluripotent stem cells

Nature communications, 2021-11, Vol.12 (1), p.6504-6504, Article 6504

2021

Link zum Volltext

Verfügbarkeit prüfen

Sphingosine-1-Phosphate Is a Novel Regulator of Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Activity

PloS one, 2015-06, Vol.10 (6), p.e0130313-e0130313

2015

Link zum Volltext

Verfügbarkeit prüfen

Early human fetal lung atlas reveals the temporal dynamics of epithelial cell plasticity

Nature communications, 2024-07, Vol.15 (1), p.5898-24, Article 5898

2024

Link zum Volltext

Verfügbarkeit prüfen

Photochemically Activated Notch Signaling Hydrogel Preferentially Differentiates Human Derived Hepatoblasts to Cholangiocytes

Advanced functional materials, 2021-01, Vol.31 (5), p.2006116-n/a

2021

Link zum Volltext

Verfügbarkeit prüfen

Orkambi® and amplifier co‐therapy improves function from a rare CFTR mutation in gene‐edited cells and patient tissue

EMBO molecular medicine, 2017-09, Vol.9 (9), p.1224-1243

2017

Link zum Volltext

Verfügbarkeit prüfen

A Therapy for Most with Cystic Fibrosis

Cell, 2020-01, Vol.180 (2), p.211-211

Bear, Christine E.

2020

Link zum Volltext

Verfügbarkeit prüfen

A Cell-Based Optimised Approach for Rapid and Efficient Gene Editing of Human Pluripotent Stem Cells

International journal of molecular sciences, 2023-06, Vol.24 (12), p.10266

2023

Link zum Volltext

Verfügbarkeit prüfen

Comparison of a novel potentiator of CFTR channel activity to ivacaftor in ameliorating mucostasis caused by cigarette smoke in primary human bronchial airway epithelial cells

Respiratory research, 2024-07, Vol.25 (1), p.269-10, Article 269

2024

Link zum Volltext

Verfügbarkeit prüfen

Viscoelastic Notch Signaling Hydrogel Induces Liver Bile Duct Organoid Growth and Morphogenesis

Advanced healthcare materials, 2022-12, Vol.11 (23), p.e2200880-n/a

2022

Link zum Volltext

Verfügbarkeit prüfen

Anti-Infectives Restore ORKAMBI ® Rescue of F508del-CFTR Function in Human Bronchial Epithelial Cells Infected with Clinical Strains of P. aeruginosa

Biomolecules (Basel, Switzerland), 2020-02, Vol.10 (2), p.334

2020

Link zum Volltext

Verfügbarkeit prüfen

Perspectives on the translation of in-vitro studies to precision medicine in Cystic Fibrosis

EBioMedicine, 2021-11, Vol.73, p.103660-103660, Article 103660

2021

Link zum Volltext

Verfügbarkeit prüfen

Conformational defects underlie proteasomal degradation of Dent's disease-causing mutants of ClC-5

Biochemical journal, 2013-06, Vol.452 (3), p.391-400

2013

Link zum Volltext

Verfügbarkeit prüfen

A new platform for high-throughput therapy testing on iPSC-derived lung progenitor cells from cystic fibrosis patients

Stem cell reports, 2021-11, Vol.16 (11), p.2825-2837

2021

Link zum Volltext

Verfügbarkeit prüfen

The CF Canada-Sick Kids Program in individual CF therapy: A resource for the advancement of personalized medicine in CF

Journal of cystic fibrosis, 2019-01, Vol.18 (1), p.35-43

2019

Link zum Volltext

Verfügbarkeit prüfen

SLC6A14, an amino acid transporter, modifies the primary CF defect in fluid secretion

eLife, 2018-07, Vol.7

2018

Link zum Volltext

Verfügbarkeit prüfen

Allele-Specific Prevention of Nonsense-Mediated Decay in Cystic Fibrosis Using Homology-Independent Genome Editing

Molecular therapy. Methods & clinical development, 2020-06, Vol.17, p.1118-1128

2020

Link zum Volltext

Verfügbarkeit prüfen

Cystic fibrosis transmembrane conductance regulator in human muscle: Dysfunction causes abnormal metabolic recovery in exercise

Annals of neurology, 2010-06, Vol.67 (6), p.802-808

2010

Link zum Volltext

Verfügbarkeit prüfen

1 – 25 von 197

Suche als RSS-Feed

Suchergebnisse filtern

Filter anzeigen

Nur zeigen

Geprüft (Peer-Review)
(193)
Mit Volltextzugriff
(185)

Publikationsform

Artikel
(195)
Buchkapitel
(2)

Sprache

Englisch
(197)
Japanisch
(37)
Latein
(1)

Erscheinungsjahr

n.n

Neu hinzugefügt

... seit 30 Tagen
(3)

Menü

Weitere Dienste

Einstellungen

Evidence for a Superoxide Permeability Pathway in Endosomal Membranes

Directed differentiation of cholangiocytes from human pluripotent stem cells

Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Potentiator VX-770 (Ivacaftor) Opens the Defective Channel Gate of Mutant CFTR in a Phosphorylation-dependent but ATP-independent Manner

ORKAMBI-Mediated Rescue of Mucociliary Clearance in Cystic Fibrosis Primary Respiratory Cultures Is Enhanced by Arginine Uptake, Arginase Inhibition, and Promotion of Nitric Oxide Signaling to the Cystic Fibrosis Transmembrane Conductance Regulator Channel

Efficient generation of functional CFTR-expressing airway epithelial cells from human pluripotent stem cells

Activity of a novel antimicrobial peptide against Pseudomonas aeruginosa biofilms

Acellular Lung Scaffolds Direct Differentiation of Endoderm to Functional Airway Epithelial Cells: Requirement of Matrix-Bound HS Proteoglycans

Generation of functional ciliated cholangiocytes from human pluripotent stem cells

Sphingosine-1-Phosphate Is a Novel Regulator of Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Activity

Early human fetal lung atlas reveals the temporal dynamics of epithelial cell plasticity

Photochemically Activated Notch Signaling Hydrogel Preferentially Differentiates Human Derived Hepatoblasts to Cholangiocytes

Orkambi® and amplifier co‐therapy improves function from a rare CFTR mutation in gene‐edited cells and patient tissue

A Therapy for Most with Cystic Fibrosis

A Cell-Based Optimised Approach for Rapid and Efficient Gene Editing of Human Pluripotent Stem Cells

Comparison of a novel potentiator of CFTR channel activity to ivacaftor in ameliorating mucostasis caused by cigarette smoke in primary human bronchial airway epithelial cells

CFTR interactome mapping using the mammalian membrane two‐hybrid high‐throughput screening system

Viscoelastic Notch Signaling Hydrogel Induces Liver Bile Duct Organoid Growth and Morphogenesis

Anti-Infectives Restore ORKAMBI ® Rescue of F508del-CFTR Function in Human Bronchial Epithelial Cells Infected with Clinical Strains of P. aeruginosa

Perspectives on the translation of in-vitro studies to precision medicine in Cystic Fibrosis

Conformational defects underlie proteasomal degradation of Dent's disease-causing mutants of ClC-5

A new platform for high-throughput therapy testing on iPSC-derived lung progenitor cells from cystic fibrosis patients

The CF Canada-Sick Kids Program in individual CF therapy: A resource for the advancement of personalized medicine in CF

SLC6A14, an amino acid transporter, modifies the primary CF defect in fluid secretion

Allele-Specific Prevention of Nonsense-Mediated Decay in Cystic Fibrosis Using Homology-Independent Genome Editing

Cystic fibrosis transmembrane conductance regulator in human muscle: Dysfunction causes abnormal metabolic recovery in exercise

Suchergebnisse filtern