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An emerging role for misfolded wild-type SOD1 in sporadic ALS pathogenesis

Frontiers in cellular neuroscience, 2013-12, Vol.7, p.253

2013

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over-oxidized form of superoxide dismutase found in sporadic amyotrophic lateral sclerosis with bulbar onset shares a toxic mechanism with mutant SOD1

Proceedings of the National Academy of Sciences - PNAS, 2012-03, Vol.109 (13), p.5074-5079

2012

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Human C9ORF72 Hexanucleotide Expansion Reproduces RNA Foci and Dipeptide Repeat Proteins but Not Neurodegeneration in BAC Transgenic Mice

Neuron (Cambridge, Mass.), 2015-12, Vol.88 (5), p.902-909

2015

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Wild-type and mutant SOD1 share an aberrant conformation and a common pathogenic pathway in ALS

Nature neuroscience, 2010-11, Vol.13 (11), p.1396-1403

2010

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Axonal Transport Defects in Neurodegenerative Diseases

The Journal of neuroscience, 2009-10, Vol.29 (41), p.12776-12786

2009

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Localized thermodynamic coupling between hydrogen bonding and microenvironment polarity substantially stabilizes proteins

Nature structural & molecular biology, 2009-07, Vol.16 (7), p.684-690

2009

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Inhibition of fast axonal transport by pathogenic SOD1 involves activation of p38 MAP kinase

PloS one, 2013-06, Vol.8 (6), p.e65235

2013

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Intrinsic dynamics of an enzyme underlies catalysis

Nature, 2005-11, Vol.438 (7064), p.117-121

2005

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A yeast model of FUS/TLS-dependent cytotoxicity

PLoS biology, 2011-04, Vol.9 (4), p.e1001052-e1001052

2011

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Structural basis for mutation-induced destabilization of profilin 1 in ALS

Proceedings of the National Academy of Sciences - PNAS, 2015-06, Vol.112 (26), p.7984-7989

2015

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Enzyme Dynamics during Catalysis

Science (American Association for the Advancement of Science), 2002-02, Vol.295 (5559), p.1520-1523

2002

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Expression of ALS-PFN1 impairs vesicular degradation in iPSC-derived microglia

Nature communications, 2024-03, Vol.15 (1), p.2497-2497, Article 2497

2024

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Mouse closed head traumatic brain injury replicates the histological tau pathology pattern of human disease: characterization of a novel model and systematic review of the literature

Acta neuropathologica communications, 2021-06, Vol.9 (1), p.118-118, Article 118

2021

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Functions of FUS/TLS From DNA Repair to Stress Response: Implications for ALS

ASN Neuro, 2014-08, Vol.6 (4), p.175909141454447

2014

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Amyotrophic lateral sclerosis-linked FUS/TLS alters stress granule assembly and dynamics

Molecular neurodegeneration, 2013-08, Vol.8 (1), p.30-30, Article 30

2013

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Anti-SOD1 Nanobodies That Stabilize Misfolded SOD1 Proteins Also Promote Neurite Outgrowth in Mutant SOD1 Human Neurons

International journal of molecular sciences, 2022-12, Vol.23 (24), p.16013

2022

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ALS-linked FUS exerts a gain of toxic function involving aberrant p38 MAPK activation

Scientific reports, 2017-03, Vol.7 (1), p.115-13, Article 115

2017

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Translation dysregulation in neurodegenerative disorders

Proceedings of the National Academy of Sciences - PNAS, 2018-12, Vol.115 (51), p.12842-12844

Bosco, Daryl A.

2018

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Genetic ablation of Sarm1 attenuates expression and mislocalization of phosphorylated TDP-43 after mouse repetitive traumatic brain injury

Acta neuropathologica communications, 2023-12, Vol.11 (1), p.206-16, Article 206

2023

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Genetic determinants of amyotrophic lateral sclerosis as therapeutic targets

CNS & neurological disorders drug targets, 2010-12, Vol.9 (6), p.779

2010

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Structure and Dynamics of Pin1 During Catalysis by NMR

Journal of molecular biology, 2007-04, Vol.367 (5), p.1370-1381

2007

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Post-Translational Modification by Cysteine Protects Cu/Zn-Superoxide Dismutase from Oxidative Damage

Biochemistry (Easton), 2013-09, Vol.52 (36), p.6137-6144

2013

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Catalysis of Cis/Trans Isomerization in Native HIV-1 Capsid by Human Cyclophilin A

Proceedings of the National Academy of Sciences - PNAS, 2002-04, Vol.99 (8), p.5247-5252

2002

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Paraoxonase gene mutations in amyotrophic lateral sclerosis

Annals of neurology, 2010-07, Vol.68 (1), p.102-107

2010

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Endoplasmic reticulum stress leads to accumulation of wild-type SOD1 aggregates associated with sporadic amyotrophic lateral sclerosis

Proceedings of the National Academy of Sciences - PNAS, 2018-08, Vol.115 (32), p.8209-8214

2018

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An emerging role for misfolded wild-type SOD1 in sporadic ALS pathogenesis

over-oxidized form of superoxide dismutase found in sporadic amyotrophic lateral sclerosis with bulbar onset shares a toxic mechanism with mutant SOD1

Human C9ORF72 Hexanucleotide Expansion Reproduces RNA Foci and Dipeptide Repeat Proteins but Not Neurodegeneration in BAC Transgenic Mice

Wild-type and mutant SOD1 share an aberrant conformation and a common pathogenic pathway in ALS

Axonal Transport Defects in Neurodegenerative Diseases

Localized thermodynamic coupling between hydrogen bonding and microenvironment polarity substantially stabilizes proteins

Inhibition of fast axonal transport by pathogenic SOD1 involves activation of p38 MAP kinase

Intrinsic dynamics of an enzyme underlies catalysis

A yeast model of FUS/TLS-dependent cytotoxicity

Structural basis for mutation-induced destabilization of profilin 1 in ALS

Enzyme Dynamics during Catalysis

Expression of ALS-PFN1 impairs vesicular degradation in iPSC-derived microglia

Mouse closed head traumatic brain injury replicates the histological tau pathology pattern of human disease: characterization of a novel model and systematic review of the literature

Functions of FUS/TLS From DNA Repair to Stress Response: Implications for ALS

Amyotrophic lateral sclerosis-linked FUS/TLS alters stress granule assembly and dynamics

Anti-SOD1 Nanobodies That Stabilize Misfolded SOD1 Proteins Also Promote Neurite Outgrowth in Mutant SOD1 Human Neurons

ALS-linked FUS exerts a gain of toxic function involving aberrant p38 MAPK activation

Translation dysregulation in neurodegenerative disorders

Genetic ablation of Sarm1 attenuates expression and mislocalization of phosphorylated TDP-43 after mouse repetitive traumatic brain injury

Genetic determinants of amyotrophic lateral sclerosis as therapeutic targets

Structure and Dynamics of Pin1 During Catalysis by NMR

Post-Translational Modification by Cysteine Protects Cu/Zn-Superoxide Dismutase from Oxidative Damage

Catalysis of Cis/Trans Isomerization in Native HIV-1 Capsid by Human Cyclophilin A

Paraoxonase gene mutations in amyotrophic lateral sclerosis

Endoplasmic reticulum stress leads to accumulation of wild-type SOD1 aggregates associated with sporadic amyotrophic lateral sclerosis

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