Details

Autor(en) / Beteiligte

• Muller, M
• Hubbard, S L
• Provias, J
• Greenberg, M
• Becker, L E
• Rutka, J T

Titel

Malignant rhabdoid tumour of the pineal region

Ist Teil von

• Canadian journal of neurological sciences, 1994-08, Vol.21 (3), p.273-277

Ort / Verlag

England

Erscheinungsjahr

1994

Quelle

MEDLINE

Beschreibungen/Notizen

• A 9-month-old male presented to hospital with signs and symptoms of raised intracranial pressure. A CT scan showed obstructive hydrocephalus from a large pineal region mass lesion into which an intratumoral hemorrhage had occurred. A posterior fossa craniectomy and subtotal excision of the mass lesion were performed. By histopathology, the lesion was a malignant rhabdoid tumour (MRT). Despite surgery and chemotherapy, the tumour grew inexorably, and the patient died four months after the initial diagnosis. MRT is a rare and highly invasive neoplasm which infrequently arises from the central nervous system. This is the first documented case of a MRT arising from the pineal region. The clinical, radiographic, and pathological features of the MRT in this patient are presented.