Details

Autor(en) / Beteiligte

• Ripoll, Juan G
• Ritter, Matthew J
• Comfere, Thomas B
• Smith, Mark M
• Schaff, Hartzell V
• Gilkey, George D
• Warner, Matthew A

Titel

Undiagnosed Systemic Mastocytosis Presenting as Postoperative Distributive Shock: A Case Report

Ist Teil von

• A&A practice, 2019-11, Vol.13 (10), p.392-395

Ort / Verlag

United States

Erscheinungsjahr

2019

Quelle

MEDLINE

Beschreibungen/Notizen

• Systemic mastocytosis (SM) is a rare clinical condition resulting from a clonal proliferation of abnormal mast cells. The clinical presentation may vary from mild cutaneous manifestations to aggressive systemic symptoms including intermittent episodes of anaphylaxis. We present a case of a 69-year-old male with abrupt and recurrent episodes of anaphylaxis with refractory distributive shock following cardiac surgery with cardiopulmonary bypass. Following a complex postoperative course, a bone marrow biopsy ultimately confirmed the diagnosis. Although rare, SM should be considered in the differential diagnosis of postoperative patients with unexplained and recurrent episodes of distributive shock.