Details

Autor(en) / Beteiligte

• Bichakjian, Christopher K
• Olencki, Thomas
• Alam, Murad
• Andersen, James S
• Berg, Daniel
• Bowen, Glen M
• Cheney, Richard T
• Daniels, Gregory A
• Glass, L Frank
• Grekin, Roy C
• Grossman, Kenneth
• Ho, Alan L
• Lewis, Karl D
• Lydiatt, Daniel D
• Morrison, William H
• Nehal, Kishwer S
• Nelson, Kelly C
• Nghiem, Paul
• Perlis, Clifford S
• Shaha, Ashok R
• Thorstad, Wade L
• Tuli, Malika
• Urist, Marshall M
• Wang, Timothy S
• Werchniak, Andrew E
• Wong, Sandra L
• Zic, John A
• McMillian, Nicole
• Hoffman, Karin
• Ho, Maria

Titel

Dermatofibrosarcoma protuberans, version 1.2014

Ist Teil von

• Journal of the National Comprehensive Cancer Network, 2014-06, Vol.12 (6), p.863-868

Ort / Verlag

United States

Erscheinungsjahr

2014

Quelle

MEDLINE

Beschreibungen/Notizen

• Dermatofibrosarcoma protuberans (DFSP) is an uncommon soft tissue tumor characterized by a relatively high risk of local recurrence and low risk of metastasis. The NCCN Guidelines for DFSP provide multidisciplinary recommendations on the management of patients with this rare disease. These NCCN Guidelines Insights highlight the addition of the Principles of Pathology section, which provides recommendations on the pathologic assessment of DFSP. Because DFSP can mimic other lesions, immunohistochemical studies are often required to establish diagnosis. Cytogenetic testing for the characteristic translocation t(17;22)(q22;q13) can also be valuable in the differential diagnosis of DFSP with other histologically similar tumors.