Details

Autor(en) / Beteiligte

• Vishnevskiĭ, A A
• Nikoladze, G D
• Romanov, Iu V

Titel

Familial bullous disease of the lungs as a cause of spontaneous pneumothorax

Ist Teil von

• Grudnaia i serdechno-sosudistaia khirurgiia, 1990 (6), p.44

Ort / Verlag

Russia (Federation)

Erscheinungsjahr

1990

Quelle

MEDLINE

Beschreibungen/Notizen

• Problems of surgical treatment of familial spontaneous pneumothorax, which is a manifestation of a hereditary form of bullous disease of the lungs, are discussed. Study of 2 families showed that the disease is inherited according to the autosome-dominant type with incomplete penetrance and/or variation expressivity. Operation was performed on 5 of 9 patients. Bullectomy and pleurodesis by means of parietal pleurectomy were conducted. Follow-up for periods of 1 to 27 years showed surgical treatment to be effective.