Details

Autor(en) / Beteiligte

• Maselli, Enrico
• Prete, Fernando

Titel

Carney's syndrome: a case report

Ist Teil von

• Chirurgia italiana, 2004-07, Vol.56 (4), p.579

Ort / Verlag

Italy

Erscheinungsjahr

2004

Quelle

MEDLINE

Beschreibungen/Notizen

• The peculiar aspects of the clinico-pathological picture and surgical treatment of Carney's syndrome, a rare morbid association of multiple non-epithelial neoplasms of the stomach, lung and chromaffin tissue, are focused on and discussed on the basis of the observation of a clinical case. The patient was a 22-year-old male with a multiple stromal tumour of the stomach, oesophageal leiomyoma, a left thoracic terato-chondroid neoplasm and gallbladder adenomyoma, surgically treated in two stages: laparotomy for gastric resection and cholecystectomy followed by left thoracotomy for resection of the intrathoracic neoplasm and excision of the oesophageal leiomyoma. The postoperative course was characterised by low morbidity and healing was monitored by means of thorough follow-up examinations. The case reported here is classed among the variants of Carney's classical triad. A knowledge of the pathological associations of these uncommon tumours and their natural history is of great importance for implementing appropriate diagnostic and therapeutic protocols.