Details

Autor(en) / Beteiligte

• Muller, John N.
• Shetye, Pradip R.
• Flores, Roberto L.

Titel

LeFort III/I for Beckwith–Wiedemann Syndrome: A Case Report

Ist Teil von

• The Cleft palate-craniofacial journal, 2023-10, Vol.60 (10), p.1342-1347

Ort / Verlag

Los Angeles, CA: SAGE Publications

Erscheinungsjahr

2023

Link zum Volltext

Quelle

Alma/SFX Local Collection

Beschreibungen/Notizen

• This case presents a facially mature patient with Beckwith–Wiedemann Syndrome (BWS) who presented with severe class III malocclusion. Computed tomography imaging revealed an anterior crossbite of 19 mm and a narrow pharyngeal airway at the level of the tongue base precluding mandibular setback surgery. The patient was indicated for a LeFort III combined with a LeFort I advancement, each of 10 mm, for a 20 mm combined advancement. Stable, functional occlusion was achieved without airway compromise. This novel use of the combined LeFort III/I can restore stable class I occlusion in patients with BWS at risk for tongue base airway compromise.