Details

Autor(en) / Beteiligte

• Sánchez Zahonero, Julia
• Ruiz Domínguez, José A
• Sánchez Zahonero, Sandra
• López García, M José

Titel

A very rare cause of peripheral precocious puberty in a girl: ovarian sex cord tumor with annular tubules

Ist Teil von

• Archivos argentinos de pediatría, 2017-06, Vol.115 (3), p.e179-e182

Ort / Verlag

Argentina

Erscheinungsjahr

2017

Quelle

MEDLINE

Beschreibungen/Notizen

• Sex cord tumor with annular tubules is an extremely uncommon gonadal stromal neoplasm. It represents 0.05-0.6% of all ovarian tumors, according to series. An unusual case is presented in a 6-year-old girl, detected as a result of an isosexual peripheral precocious puberty. The highlight of this case is that no mass attached to the ovary was found, but only a gonadal asymmetry without radiological signs of malignancy. After confirming the presence of tumoral cells by intraoperative biopsy, unilateral salpingo-oophorectomy with ipsilateral para-aortic and pelvic lymphadenectomy was performed. Afterwards, the evolution of the patient was favorable.