Details

Autor(en) / Beteiligte

• Kaieda, Shinjiro
• Zaizen, Yoshiaki
• Nomura, Yoriko
• Okabe, Koki
• Honda, Seiyo
• Kage, Masayoshi
• Ida, Hiroaki
• Hoshino, Tomoaki
• Fukuda, Takaaki

Titel

An autopsy case of refractory vasculo-Behçet’s disease

Ist Teil von

• Modern rheumatology, 2015-03, Vol.25 (2), p.307-311

Ort / Verlag

United States: Informa Healthcare

Erscheinungsjahr

2015

Quelle

MEDLINE

Beschreibungen/Notizen

• Abstract Pulmonary vascular involvement in Behçet’s disease is a rare complication with a poor prognosis. We present an autopsy case of vasculo-Behçet’s disease complicated by pulmonary hemorrhage, possibly caused by rupture of pulmonary artery aneurysms. The patient was treated with a combination of high-dose steroids and pulse cyclophosphamide, but he died from massive hemoptysis. This case highlights the need for potent new therapies for patients with vasculo-Behçet’s disease refractory to conventional immunosuppressive therapy, such as a combination of steroids and cyclophosphamide.