Details

Autor(en) / Beteiligte

• Siehr, Stephanie L.
• Bernstein, Daniel
• Yeh, Justin
• Berry, Gerald J.
• Rosenthal, David N.
• Hollander, Seth A.

Titel

Orthotopic heart transplantation in two infants with histiocytoid cardiomyopathy and left ventricular non‐compaction

Ist Teil von

• Pediatric transplantation, 2013-11, Vol.17 (7), p.E165-E167

Ort / Verlag

Denmark

Erscheinungsjahr

2013

Link zum Volltext

Quelle

Wiley Online Library - AutoHoldings Journals

Beschreibungen/Notizen

• HC is a rare cause of congestive heart failure that typically presents with malignant ventricular arrhythmias in infants, often requiring urgent intervention. Successful heart transplantation in a patient with HC has only been reported once (J Heart Lung Transplant 2004: 23: 902). The combination of HC with concurrent LVNC has only been described three times (Int J Legal Med 2009: 123: 47; Hum Pathol 2005: 36: 403; Pediatr Dev Pathol 2012: 15: 397). We report two rare cases of HC with LVNC in two infants presenting with cardiogenic shock, one requiring ECMO support who was successfully bridged to orthotopic heart transplantation with a Berlin Heart LVAD.