Details

Autor(en) / Beteiligte

• Recuero Díaz, José Luis
• Embún Flor, Raúl
• Menal Muñoz, Patricia
• Hernández Ferrández, Jorge
• Arrarás Martínez, Miguel Jesús
• Rivas de Andrés, Juan José

Titel

Thymic carcinoid associated with multiple endocrine neoplasia syndrome type I

Ist Teil von

• Archivos de bronconeumología (English ed.), 2013-03, Vol.49 (3), p.122-125

Erscheinungsjahr

2013

Quelle

Elsevier ScienceDirect Journals Complete

Beschreibungen/Notizen

• Thymic carcinoids are a rare entity that may be associated with endocrine diseases like Cushing's syndrome or multiple endocrine neoplasia syndrome type I (MEN1). These tumors represent 4% of anterior mediastinal tumors and are characterized by their very aggressive behavior. We present the case of a patient with a previous MEN 1 diagnosis in whom, during the follow up of his disease, a thoracic image compatible with thymic carcinoid was detected. After an extended thymectomy that included peri-thymic fat resection, the clinical diagnosis was confirmed. A follow up examination 14 months later revealed a suspicious lesion that suggested local recurrence, therefore the patient was reoperated on. The pathology report of this surgery indicated post-radiation fibrosis. Likewise, we present a review of the current diagnostic and therapeutic management of patients with MEN1 syndrome who are diagnosed with thymic carcinoid.