Details

Autor(en) / Beteiligte

• Weldetsadik, Abate Yeshidinber
• Kebede, Abdi
• Godu, Binyam Gebremedhin
• Gama, Maru

Titel

Unilateral pulmonary vein atresia presenting with recurrent hemoptysis and bronchial varices in an Ethiopian adolescent: a case report

Ist Teil von

• Journal of medical case reports, 2023-06, Vol.17 (1), p.246-246, Article 246

Ort / Verlag

England: BioMed Central Ltd

Erscheinungsjahr

2023

Quelle

SpringerLink Journals

Beschreibungen/Notizen

• Congenital unilateral pulmonary vein atresia is a rare anomaly resulting from failure of the pulmonary vein to incorporate in the left atrium. It is a very rare cause of recurrent respiratory infections and hemoptysis requiring a high index of suspicion for proper diagnosis and management in early childhood. We report a 13-year old Anuac (Ethiopia, Region of Gambela) male adolescent with a delayed diagnosis of isolated atresia of the left pulmonary veins despite early childhood presentation with recurrent chest infections, hemoptysis and exercise intolerance. Contrast enhanced CT of thorax with reconstructed planes confirmed the diagnosis. He underwent pneumonectomy for severe and recurrent symptoms and did well on subsequent follow ups after 6 months of pneumonectomy. Although a rare anomaly, congenital unilateral pulmonary vein atresia should be considered in the differential diagnosis of a child presenting with recurrent chest infections, exercise intolerance and hemoptysis to facilitate early appropriate diagnosis and treatment.