Details

Autor(en) / Beteiligte

• Khajali, Zahra
• Arabian, Maedeh
• Aliramezany, Maryam

Titel

Best management in isolated right ventricular hypoplasia with septal defects in adults

Ist Teil von

• Journal of cardiovascular and thoracic research, 2020-01, Vol.12 (3), p.214-220

Ort / Verlag

Tabriz: Tabriz University of Medical Sciences

Erscheinungsjahr

2020

Quelle

Electronic Journals Library

Beschreibungen/Notizen

• In right ventricular hypoplasia, a patent foramen ovale or an atrial septal defect can serve as an escape valve.1 The clinical manifestations are usually nonspecific and vary related to the degree of hypoplasia and right ventricle compliance as well as the degree of right-to-left shunting via the atrial septal defect or the patent foramen ovale. Physical examinations are often normal.2 The diagnosis and evaluation of the severity of the syndrome are routinely performed by echocardiography, cardiac magnetic resonance imaging, and hemodynamic evaluation.3 The mild hypoplasia of the right ventricle can be corrected by atrial septal defect closure; nevertheless, for subjects with severe hypoplasia, the Glenn shunt, one and half ventricle repair, or even the Fontan surgery should be chosen.4 This report describes the history, para-clinical data, and management of 6 patients with isolated RVH treated medically or surgically based on their symptoms. According to the cardiac magnetic resonance results, the right ventricle volume was in the lower normal limit with a mildly reduced function (Figure 2A). [...]the atrial septal defect was closed with an Occlutech® device (21 mm) percutaneously.